Pneumological discussion

This was a typical case of CPFE. The clinical data were suggestive of the diagnosis:
  1. Male
  2. Ex-smoker (of >40 pack-years)
  3. Severe dyspnoea
  4. Functional airway obstruction with preserved lung volumes
  5. Impaired carbon monoxide diffusing capacity
  6. Hypoxaemia at exercise
  7. Indirect signs of pulmonary hypertension