The MSCT shows signs of emphysema and pulmonary fibrosis with possible UIP pattern, i.e. combined pulmonary fibrosis and emphysema
The differential diagnosis includes the following:
- Idiopathic interstitial pneumonia with emphysema, ie. CPFE
- Connective tissue disease-associated CPFE
- Cottin V, et al. Combined pulmonary fibrosis and emphysema syndrome in connective tissue disease. Arthritis Rheum. 2011;63(1):295-304.
- Cottin V. The impact of emphysema in pulmonary fibrosis. Eur Respir Rev. 2013;22(128):153-157.