The 2011 guideline of the American Thoracic Society/European Respiratory Society/Japanese Respiratory Society/Latin American Thoracic Society (ATS/ERS/JRS/ALAT) established multidisciplinary team (MDT) approach for the diagnosis of IPF where clinical, functional, radiological and (if available), pathology data are discussed.

An important part of the diagnosis is HRCT with a typical pattern, the so-called Usual Interstitial Pneumonia (UIP) pattern. This pattern can, however, have several differential diagnoses. 

  1. Raghu G, et al. An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: Evidence-based guidelines for diagnosis and management. Am J Respir Crit Care Med 2011;183(6):788-824.
  2. Sverzellati N. Highlights of HRCT imaging in IPF. Respiratory Research. 2013;14(Suppl1):S3 
Provided by Prof. Heussel and PD Kreuter (Thoraxklinik Heidelberg, Germany)