Idiopathic pulmonary fibrosis (IPF) is a chronic lung disease of the elderly with progressive fibrosis of the lung parenchyma and a median survival between 3-5 years.
Typical symptoms include dyspnoea on exertion and dry cough. At auscultation, in most patients the typical lung sound “velcro” crackles can be found. The course of the disease is very variable from slow progression over many years to rapid decline of lung function and early death.
Poletti V, et al. Idiopathic Pulmonary Fibrosis: Diagnosis and prognostic evaluation. Respiration. 2013;86:5-12.